[Papillon-Lefevre syndrome: a case report].

[papillon-lefèvre syndrome]

Papillon-Lefevre syndrome (PLS ) is an extremely rare inherited disease as an autosomal recessive trait . The disorder is characterized by diffuse palmoplantar keratoderma and premature loss of both deciduous and permanent teeth . This paper described a case of PLS with classic clinical features and briefly reviewed the relevant literature .