Rare Diseases Symptoms Automatic Extraction

Malignant atrophic papulosis (Degos' syndrome).

[malignant atrophic papulosis]

A 29-year-old Japanese man with malignant atrophic papulosis had a 1-year history of scattered, asymptomatic, whitish or skin-colored papules, as well as erythematous papules with central atrophy showing a porcelain-like appearance on the trunk and extremities. Histologic examination revealed lymphocyte-mediated necrotizing vasculitis with considerable deposition of mucin in the dermis. The wedge-shaped necrosis of the dermis was not detected. Based on a review of the literature we think that this case represents the histologic features of the early skin lesions of malignant atrophic papulosis.

Diseases presenting "vasculitis" symptom

  • coats disease
  • dracunculiasis
  • dystrophic epidermolysis bullosa
  • erdheim-chester disease
  • erythropoietic protoporphyria
  • familial mediterranean fever
  • focal myositis
  • inclusion body myositis
  • malignant atrophic papulosis
  • papillon-lefèvre syndrome
  • pyruvate dehydrogenase deficiency
  • scrub typhus
  • sneddon syndrome
  • typhoid
  • waldenström macroglobulinemia

This symptom has already been validated