Wolf-Hirschhorn syndrome; oro-dental manifestations and management.

[wolf-hirschhorn syndrome]

The major manifestations of the Wolf-Hirschhorn syndrome are developmental delay , short stature , mental impairment and epilepsy . Clefts of the lip and palate are sometimes present . Dental problems which are overshadowed by the major syndromic manifestations warrant appropriate management . We have documented an affected South African boy , discussed his dental management and reviewed the oro-dental implications of the disorder .