A case report: nasobiliary drainage inducing remission in benign recurrent intrahepatic cholestasis.

[benign recurrent intrahepatic cholestasis]

Benign recurrent intrahepatic cholestasis is a rare hereditary disorder characterized by recurrent episodes of cholestasis and pruritus without anatomical obstruction . Generally , medical therapy is not effective in benign recurrent intrahepatic cholestasis . Here , we report the case of a young male patient with benign recurrent intrahepatic cholestasis who presented with cholestatic jaundice and pruritus , refractory to standard therapies . He improved on treatment with temporary endoscopic nasobiliary drainage . We propose that temporary endoscopic nasobiliary drainage should be considered in cholestatic benign recurrent intrahepatic cholestasis patients . A 36 -year -old male patient admitted to our outpatient clinic with the complaint of pruritus . His anamnesis revealed that he experienced the same symptoms and signs in 2006 . He was hospitalized in a hepatology clinic and was thoroughly examined . Liver biopsy was performed , and he was finally diagnosed as having benign recurrent intrahepatic cholestasis . Medical therapy options all proved to be ineffective and we were able to achieve remission in this patient only with the help of nasobiliary drainage . For this patient , we tried nasobiliary drainage in addition to the standard medical therapies . He improved on nasobiliary drainage . In conclusion , we propose that temporary endoscopic biliary drainage should be considered in cholestatic benign recurrent intrahepatic cholestasis patients . We hope that this case report contributes to the topic , since only a few nasobiliary drainage case experiences have been reported to date .

Diseases
Validation

Diseases presenting "rare hereditary disorder" symptom

benign recurrent intrahepatic cholestasis

child syndrome

erythropoietic protoporphyria

kindler syndrome

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