Rare Diseases Symptoms Automatic Extraction
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Primary mesenchymal tumors of the pancreas: single-center experience over 16 years.
[well-differentiated liposarcoma]
Primary
mesenchymal
tumors
of
the
pancreas
are
extremely
rare
and
no
comprehensive
study
of
this
class
of
tumors
has
been
previously
performed
.
Twenty
cases
of
the
primary
mesenchymal
tumors
of
the
pancreas
were
selected
and
compared
clinicopathologic
variables
with
consecutively
resected
500
pancreatic
ductal
adenocarcinomas
.
Finally
,
20
(
0
.
3
%
)
cases
were
confirmed
as
primary
mesenchymal
tumors
.
The
14
(
70
%
)
cases
of
benign
/
borderline
tumors
included
4
cases
of
fibromatoses
,
2
cases
of
cavernous
hemangiomas
,
2
cases
of
schwannomas
,
2
cases
of
solid
and
cystic
hamartomas
,
2
cases
of
solitary
fibrous
tumors
,
1
case
of
inflammatory
myofibroblastic
tumor
,
and
1
case
of
angiomyolipoma
.
The
6
(
30
%
)
cases
of
sarcomas
comprised
3
cases
of
undifferentiated
/
unclassified
sarcomas
,
1
case
of
leiomyosarcoma
,
1
case
of
Ewing
sarcoma
/
primitive
neuroectodermal
tumor
,
and
1
case
of
atypical
lipomatous
tumor
/
well-differentiated
liposarcoma
.
When
compared
with
the
500
ductal
adenocarcinomas
,
the
3
surgically
resected
sarcomas
were
larger
(
mean
,
5
.
8
cm
vs
3
.
6
cm
;
P
=
0
.
02
)
;
however
,
no
difference
in
median
survival
time
was
observed
between
patients
with
sarcoma
(
23
months
)
and
patients
with
ductal
adenocarcinoma
(
16
months
)
.
First
,
primary
mesenchymal
tumors
of
the
pancreas
are
extremely
rare
.
Second
,
several
primary
mesenchymal
tumor
types
can
be
observed
in
the
pancreas
.
Understanding
these
rare
disease
entities
will
help
ensure
their
correct
diagnosis
.
Diseases
Validation
Diseases presenting
"leiomyosarcoma"
symptom
adrenal incidentaloma
alpha-thalassemia
dedifferentiated liposarcoma
focal myositis
liposarcoma
pleomorphic liposarcoma
well-differentiated liposarcoma
This symptom has already been validated