A case of Allgrove (Triple A) syndrome associated with renal ectopia.

[triple a syndrome]

Allgrove syndrome (triple-A syndrome ) is an autosomal recessive disorder characterized by adrenocorticotropin hormone-resistant adrenal insufficiency , achalasia and alacrima . Aside from the classic features of the syndrome , several abnormalities including mainly neurological abnormalities have been reported in the syndrome . Herein , we presented a case of Allgrove syndrome associated with left renal ectopla . To the best of our knowledge renal abnormality in Allgrove syndrome has not been reported in the literature until now . We think that ectopic kidney diagnosed in our patient is coincidental because the incidence of renal ectopia is high , approximately 1 in 900 in population .