Rare Diseases Symptoms Automatic Extraction

A case of rapidly fatal systemic capillary leak syndrome in a kidney transplant recipient.

[systemic capillary leak syndrome]

Idiopathic Systemic Capillary Leak Syndrome (SCLS) is a rare entity characterised by idiopathic increasing of capillary permeability associated with recurrent attacks of hypovolaemic shock. We report the case of a 39-year-old man with a SCLS fourteen years after a cadaveric renal transplantation. The clinical evolution was rapidly fatal despite treatment with corticoids, aminophylline and terbutaline which are the most efficient drugs known to prevent attacks.

Diseases presenting "recurrent attacks" symptom

  • allergic bronchopulmonary aspergillosis
  • benign recurrent intrahepatic cholestasis
  • erythropoietic protoporphyria
  • familial mediterranean fever
  • neuralgic amyotrophy
  • systemic capillary leak syndrome

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