[Idiopathic capillary hyperpermeability syndrome revealing of Waldenström disease].

[systemic capillary leak syndrome]

Waldenstrom disease is a rare hematologic disorder characterized by lymphoplasmacytic proliferation associated with the production of monoclonal IgM . Visceral injuries are described but some are rare (lung ), others never reported (cardiac ). We report for information and discussion a case representing these particular situations , considering that these attacks were revealing . It is a 63 year old man who was admitted to the emergency room in an array of tamponade , with edema at the front and four members . Clinical and radiological examinations were objectified bilateral pleural effusion , ascite and pericarditis . The biological exploration showed pancytopenia , serum proteins 120 g /L and a monoclonal peak migrant beta 2 globulin electrophoresis which is made by monoclonal immunoglobulin M (IgM kappa ). The bone marrow confirmed the diagnosis of the Waldenström disease . This is a mode of revelation never described before . Considering this case , it would be wise to think of a Waldenström disease before any polyserositis .