Intraventricular hemorrhage as an unusual presenting form of Sneddon syndrome.

[sneddon syndrome]

Intraventricular hemorrhage , which has a poor prognosis , is an extremely rare presenting symptom of central nervous system vasculitis . Sneddon syndrome , which is a systemic vasculitic disease , generally presents with ischemic stroke and livedo reticularis . Intraventricular hemorrhage is extremely rare in Sneddon syndrome and has not been reported as the presenting complaint .We report a 37 -year -old woman who presented with acute intraventricular hemorrhage , and on further evaluation her condition was diagnosed as Sneddon syndrome .Patient underwent ventriculoperitoneal shunting operation for hydrocephalus and her condition markedly improved 6 months later ; she was independent in her activities of daily living .In this report , we emphasize the importance of multisystemic evaluation of patients , especially those with obscure angiography findings .

Diseases
Validation

Diseases presenting "hydrocephalus" symptom

achondroplasia

alexander disease

canavan disease

congenital toxoplasmosis

harlequin ichthyosis

hirschsprung disease

homocystinuria without methylmalonic aciduria

hydrocephalus with stenosis of the aqueduct of sylvius

krabbe disease

monosomy 21

proteus syndrome

severe combined immunodeficiency

sneddon syndrome

von hippel-lindau disease

wiskott-aldrich syndrome

This symptom has already been validated