Intraventricular hemorrhage as an unusual presenting form of Sneddon syndrome.

[sneddon syndrome]

Intraventricular hemorrhage , which has a poor prognosis , is an extremely rare presenting symptom of central nervous system vasculitis . Sneddon syndrome , which is a systemic vasculitic disease , generally presents with ischemic stroke and livedo reticularis . Intraventricular hemorrhage is extremely rare in Sneddon syndrome and has not been reported as the presenting complaint .We report a 37 -year -old woman who presented with acute intraventricular hemorrhage , and on further evaluation her condition was diagnosed as Sneddon syndrome .Patient underwent ventriculoperitoneal shunting operation for hydrocephalus and her condition markedly improved 6 months later ; she was independent in her activities of daily living .In this report , we emphasize the importance of multisystemic evaluation of patients , especially those with obscure angiography findings .