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Periodontal findings and other oral manifestations in Proteus syndrome: a case report.
[proteus syndrome]
Proteus
syndrome
is
an
extremely
rare
congenital
disorder
with
progressive
asymmetric
overgrowth
of
multiple
tissues
.
The
etiology
is
unknown
to
date
.
The
aim
of
this
article
was
to
describe
the
clinical
and
radiographic
periodontal
findings
and
other
oral
manifestations
in
a
patient
with
Proteus
syndrome
.
A
13
-
year
-old
Caucasian
Brazilian
girl
with
Proteus
syndrome
was
evaluated
by
means
of
clinical
examination
and
full-mouth
intraoral
radiographic
analysis
.
The
patient
showed
skeletal
malformations
;
gigantism
;
facial
phenotype
;
and
overgrowth
of
multiple
tissues
,
including
disproportionate
overgrowth
of
skull
,
left
hand
,
and
lower
limbs
.
Evaluation
of
the
plantar
surface
of
the
left
foot
showed
cerebriform
connective
nevus
.
The
hands
also
showed
reduced
range
of
motion
.
Intraoral
examination
revealed
enamel
hypoplasia
of
permanent
teeth
restricted
to
the
left
side
of
the
mouth
,
generalized
gingival
overgrowth
,
abundant
dental
plaque
,
and
malpositioned
teeth
.
Neither
periodontal
pockets
nor
alveolar
bone
destruction
were
detected
.
In
conclusion
,
oral
manifestations
of
Proteus
syndrome
may
include
gingival
overgrowth
and
malposition
of
teeth
,
as
well
as
unilateral
enamel
hypoplasia
,
as
shown
in
this
case
report
.
