Rare Diseases Symptoms Automatic Extraction
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Papillon-Lefevre syndrome.
[papillon-lefèvre syndrome]
Papillon-
Lefevre
syndrome
is
a
very
rare
syndrome
of
autosomal
recessive
inheritance
characterized
by
palmoplanter
hyperkeratosis
of
the
skin
and
severe
periodontal
disease
extending
to
destruction
of
the
alveolar
bone
surrounding
deciduous
and
permanent
teeth
as
they
erupt
leading
to
precocious
loss
of
dentition
.
Although
the
exact
pathogenesis
of
this
syndrome
is
still
unknown
immunologic
,
microbiologic
,
and
genetic
bases
have
been
proposed
.
Here
we
report
a
case
of
Papillon-
Lefevre
syndrome
.
The
patient
had
generalized
plaque
accumulation
along
with
halitosis
,
mobile
teeth
with
periodontal
pocket
with
pus
exudation
.
Blood
&
biochemical
report
was
within
normal
limit
with
a
low
CD
3
+
and
CD
4
+
.
