Rare Diseases Symptoms Automatic Extraction
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A random Abstract
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Palmoplantar keratoderma with progressive gingivitis and recurrent pyodermas.
[papillon-lefèvre syndrome]
Papillon-
Lefèvre
syndrome
(
PLS
)
is
a
rare
inherited
palmoplantar
keratoderma
(
PPK
)
that
is
associated
with
progressive
gingivitis
and
recurrent
pyodermas
.
We
present
a
case
exhibiting
classic
features
of
this
autosomal-recessive
condition
and
review
the
current
understanding
of
its
pathophysiology
,
diagnosis
,
and
treatment
.
Additionally
,
a
review
of
pertinent
transgredient
PPKs
is
undertaken
,
with
key
and
distinguishing
features
of
each
syndrome
highlighted
.
