Megacystis-microcolon-intestinal hypoperistalsis syndrome.

[megacystis-microcolon-intestinal hypoperistalsis syndrome]

The megacystis-microcolon -intestinal hypoperistalsis syndrome is a congenital disorder characterized by urinary bladder distension and hypoperistalsis throughout the entire gastrointestinal tract . We present a new case with the typical clinical , radiological , and pathological findings of the syndrome . The diagnosis should be suspected in a patient who present clinically with intestinal obstruction and urinary retention , and confirmed with imaging studies , including abdominal plain films , urinary tract ultrasonography , and contrast studies of the colon and the bladder . The prognosis is generally very poor . Our patient died secondary to sepsis on day 5 of life .