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Understanding pediatric intestinal pseudo-obstruction: implications for nurses.
[megacystis-microcolon-intestinal hypoperistalsis syndrome]
Pseudo-obstruction
is
actually
a
group
of
disorders
resulting
in
bowel
dysmotility
in
the
absence
of
anatomic
obstruction
.
Because
of
varied
pathologic
abnormalities
of
the
GI
tract
involved
in
the
disorder
,
pseudo-obstruction
has
been
reported
in
the
literature
under
different
names
,
including
hypoganglionosis
,
chronic
adynamic
ileus
,
pseudo-
Hirschprung
's
disease
,
visceral
neuropathy
,
visceral
myopathy
,
and
megacystis-
microcolon
-
intestinal
hypoperistalsis
syndrome
.
Although
a
rare
condition
,
its
effects
are
severe
,
disabling
,
and
life-threatening
in
pediatric
clients
.
Prognosis
is
inversely
correlated
with
age
and
is
especially
poor
in
those
children
with
symptoms
as
newborns
.
Management
involves
promoting
nutrition
adequate
for
growth
,
treating
symptoms
,
and
preventing
complications
.
Total
parenteral
nutrition
is
almost
always
required
,
and
its
long
-term
use
is
associated
with
chronic
cholestasis
and
potential
hepatic
failure
.
Nurses
may
encounter
pediatric
clients
with
this
disorder
and
their
families
in
many
different
healthcare
arenas
,
such
as
in
radiology
departments
,
ambulatory
care
,
and
acute
and
home
care
settings
.
The
purpose
of
this
article
is
to
review
current
literature
on
this
disease
and
summarize
information
useful
to
nurses
.
Diseases
Validation
Diseases presenting
"visceral myopathy"
symptom
megacystis-microcolon-intestinal hypoperistalsis syndrome
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