Megacystis microcolon intestinal hypoperistalsis syndrome with bilateral duplicated systems.

[megacystis-microcolon-intestinal hypoperistalsis syndrome]

A 29 -year -old multigravida woman presented for her second prenatal ultrasound evaluation at 30 weeks of gestation . The study showed a female fetus , bilateral duplicated systems with severe hydronephrosis in the upper pole moieties and a massively distended bladder . Initial interpretation suggested ectopic /obstructing bilateral ureteroceles . To evaluate these findings further , a prenatal magnetic resonance imaging scan was obtained , documenting the absence of ureteroceles . The presumptive diagnosis of megacystis microcolon intestinal hypoperistalsis syndrome was made . After birth , contrast enema confirmed the presence of microcolon . This appears to be the first reported case of megacystis microcolon intestinal hypoperistalsis syndrome with bilateral duplex systems evaluated with prenatal magnetic resonance imaging .