Megacystis microcolon intestinal hypoperistalsis syndrome.

[megacystis-microcolon-intestinal hypoperistalsis syndrome]

Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS ) is a rare and the most severe form of functional intestinal obstruction in the newborn . The major features of this congenital and usually lethal anomaly are abdominal distension , bile-stained vomiting , and absent or decreased bowel peristalsis . Abdominal distension is a consequence of the distended , unobstructed urinary bladder with or without upper urinary tract dilation . Most patients with MMIHS are not able to void spontaneously . This article reviews the pathogenesis of MMIHS as well as the clinical , radiological , surgical and histological findings in all reported cases of this syndrome .