Malignant atrophic papulosis (Degos' syndrome).

[malignant atrophic papulosis]

A 29 -year -old Japanese man with malignant atrophic papulosis had a 1 -year history of scattered , asymptomatic , whitish or skin -colored papules , as well as erythematous papules with central atrophy showing a porcelain-like appearance on the trunk and extremities . Histologic examination revealed lymphocyte-mediated necrotizing vasculitis with considerable deposition of mucin in the dermis . The wedge-shaped necrosis of the dermis was not detected . Based on a review of the literature we think that this case represents the histologic features of the early skin lesions of malignant atrophic papulosis .