Rare Diseases Symptoms Automatic Extraction
Home
A random Abstract
Our Project
Our Team
Benign cutaneous Degos' disease.
[malignant atrophic papulosis]
Malignant
atrophic
papulosis
is
a
rare
systemic
vaso-occlusive
disorder
characterized
by
thrombosis
of
vessels
of
the
dermis
,
gastrointestinal
tract
,
central
nervous
system
and
,
occasionally
,
other
organs
.
Cutaneous
lesions
consist
of
erythematous
,
dome-shaped
papules
that
develop
a
central
area
of
necrosis
to
leave
a
porcelain-like
scar
.
The
most
accepted
theory
of
pathogenesis
is
based
on
endothelial
cell
damage
.
There
is
no
effective
treatment
of
the
disease
.
We
describe
a
26
-
year
-old
man
with
Degos
'
disease
,
a
diagnosis
based
on
the
clinical
and
histologic
pattern
of
skin
lesions
.
The
good
response
to
antiplatelet
therapy
and
the
absence
of
systemic
involvement
over
8
years
'
follow-up
is
noteworthy
.
We
believe
that
this
case
represents
the
benign
form
of
the
disease
,
typically
referred
to
as
benign
cutaneous
Degos
'
disease
.
Diseases
Validation
Diseases presenting
"accepted theory of pathogenesis is based on endothelial"
symptom
malignant atrophic papulosis
You can validate or delete this automatically detected symptom
Validate the Symptom
Delete the Symptom
