A case of systemic malignant atrophic papulosis (KÃ¶hlmeier-Degos' disease).

[malignant atrophic papulosis]

Malignant atrophic papulosis (MAP ) is a rare and clinically distinctive vasculopathy . It is characterized by narrowing and occlusion of the lumen by intimal proliferation and thrombosis , which leads to ischemia and infarction in the involved organ systems . Its rarity and rapidly fatal course make the disease a difficult diagnostic and therapeutic challenge .