Rare Diseases Symptoms Automatic Extraction
Home
A random Abstract
Our Project
Our Team
Wegener's granulomatosis: a new entity in the growing differential diagnosis of Degos' disease.
[malignant atrophic papulosis]
Wegener
's
granulomatosis
(
WG
)
is
a
multisystemic
vasculitis
,
with
skin
involvement
in
14
%
of
cases
and
with
palpable
purpura
,
subcutaneous
nodules
and
necrotic
papules
as
the
common
features
.
(
1
)
We
present
a
patient
diagnosed
with
WG
who
had
multiple
whitish
papules
similar
to
those
of
malignant
atrophic
papulosis
(
Degos
'
disease
)
,
which
appeared
during
a
flare
of
his
disease
.
Lesions
of
malignant
atrophic
papulosis
are
said
to
be
pathognomonic
;
nevertheless
,
various
diseases
with
similar
clinical
lesions
have
been
described
.
To
our
knowledge
,
this
is
the
first
reported
case
of
such
lesions
in
a
patient
with
WG
,
and
we
suggest
WG
should
be
included
in
the
differential
diagnosis
of
Degos
'
disease
.
Diseases
Validation
Diseases presenting
"vasculitis"
symptom
coats disease
dracunculiasis
dystrophic epidermolysis bullosa
erdheim-chester disease
erythropoietic protoporphyria
familial mediterranean fever
focal myositis
inclusion body myositis
malignant atrophic papulosis
papillon-lefèvre syndrome
pyruvate dehydrogenase deficiency
scrub typhus
sneddon syndrome
typhoid
waldenström macroglobulinemia
This symptom has already been validated
