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Degos disease: a new simulator of non-accidental injury.
[malignant atrophic papulosis]
Recent
high
-profile
cases
have
made
paediatricians
very
aware
of
the
serious
implications
of
either
missing
or
wrongly
diagnosing
non-accidental
injury
.
Subdural
fluid
collections
in
non-mobile
infants
usually
represent
haemorrhage
caused
by
non-accidental
injury
.
We
report
a
6
-
month
-old
male
who
presented
to
the
Accident
and
Emergency
Department
of
Birmingham
Heartlands
Hospital
with
bilateral
subdural
fluid
collections
and
skin
ulcers
resembling
cigarette
burns
.
Non-accidental
injury
was
considered
to
be
the
most
likely
diagnosis
.
However
,
while
under
observation
in
hospital
,
the
child
's
neurological
condition
deteriorated
with
progressive
cerebral
infarctions
,
and
serial
photographs
of
the
skin
lesions
showed
failure
to
heal
.
The
revised
diagnosis
,
confirmed
histologically
,
was
Degos
disease
,
an
extremely
rare
and
often
fatal
occlusive
vasculopathy
.
The
child
was
treated
palliatively
and
died
8
weeks
after
presentation
.
This
report
informs
doctors
of
a
new
simulator
of
non-accidental
injury
to
be
considered
in
infants
with
otherwise
unexplained
subdural
fluid
collections
.