A case of Degos disease successfully treated with corticosteroid combined with cyclophosphamide.

[malignant atrophic papulosis]

Degos disease is a rare disorder characterized by systemic vasculitis involving various organs . There is no established , effective treatment for the disorder , and its prognosis is still poor . Combination therapy with corticosteroid and cyclophosphamide is considered effective for vasculitides involving the small arteries such as ANCA-associated vasculitis . We present here a 42 -year -old man who developed Degos disease over several months , and was successfully treated using combined treatment with corticosteroid and cyclophosphamide .

Diseases
Validation

Diseases presenting "vasculitis" symptom

coats disease

dracunculiasis

dystrophic epidermolysis bullosa

erdheim-chester disease

erythropoietic protoporphyria

familial mediterranean fever

focal myositis

inclusion body myositis

malignant atrophic papulosis

papillon-lefèvre syndrome

pyruvate dehydrogenase deficiency

scrub typhus

sneddon syndrome

typhoid

waldenström macroglobulinemia

This symptom has already been validated