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Malignant atrophic papulosis: a case report with severe visual and neurological impairment.
[malignant atrophic papulosis]
Malignant
atrophic
papulosis
,
or
Degos
'
disease
,
is
a
severe
systemic
vasculopathy
extremely
rare
in
children
.
The
skin
,
gastrointestinal
tract
,
and
central
nervous
system
are
most
frequently
affected
.
We
report
a
5
-
year
-old
girl
with
malignant
atrophic
papulosis
who
presented
with
widespread
skin
lesions
from
early
infancy
and
severe
visual
and
neurological
impairment
.
Diseases
Validation
Diseases presenting
"gastrointestinal tract"
symptom
benign recurrent intrahepatic cholestasis
carcinoma of the gallbladder
cowden syndrome
cutaneous mastocytosis
dedifferentiated liposarcoma
epidermolysis bullosa simplex
erdheim-chester disease
esophageal adenocarcinoma
esophageal carcinoma
familial mediterranean fever
hirschsprung disease
malignant atrophic papulosis
megacystis-microcolon-intestinal hypoperistalsis syndrome
proteus syndrome
pyomyositis
triple a syndrome
waldenström macroglobulinemia
well-differentiated liposarcoma
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