Rare Diseases Symptoms Automatic Extraction
Home
A random Abstract
Our Project
Our Team
Degos disease with dermatomyositis-like phenomenon: a diagnostic dilemma and a therapeutic challenge.
[malignant atrophic papulosis]
Degos
disease
is
a
type
of
vasculopathy
characterized
by
progressive
occlusion
of
small
-sized
blood
vessels
primarily
involving
the
skin
,
gastrointestinal
system
,
and
central
nervous
system
as
well
as
various
other
systems
.
Owing
to
the
rarity
of
the
condition
,
the
diagnosis
is
often
a
challenge
;
consequently
,
management
is
even
more
difficult
owing
to
the
paucity
of
experience
and
literature
for
the
effective
treatment
of
this
entity
.
We
report
a
case
of
a
50
-
year
-old
male
patient
with
classic
skin
lesions
and
rapidly
progressive
fatal
clinical
course
involving
multiple
organs
associated
with
dermatomyositis
-like
features
.
Therapeutic
challenge
in
such
a
case
of
secondary
Degos
disease
with
multiorgan
dysfunction
is
discussed
.
Secondary
Degos
disease
with
underlying
multisystem
dysfunction
is
a
rapidly
fatal
disease
.
The
patient
must
be
thoroughly
investigated
to
watch
for
systemic
involvement
and
aggressively
treated
preferably
with
antiplatelet
drugs
and
immunosuppresants
so
as
to
moderate
the
severity
of
the
disease
.
Corticosteroids
are
best
avoided
to
prevent
gastrointestinal
perforation
.
Diseases
Validation
Diseases presenting
"skin lesions"
symptom
child syndrome
cowden syndrome
cutaneous mastocytosis
cystinuria
dystrophic epidermolysis bullosa
epidermolysis bullosa simplex
erdheim-chester disease
erythropoietic protoporphyria
familial mediterranean fever
focal myositis
gm1 gangliosidosis
heparin-induced thrombocytopenia
hirschsprung disease
junctional epidermolysis bullosa
lamellar ichthyosis
liposarcoma
lymphangioleiomyomatosis
malignant atrophic papulosis
oligodontia
omenn syndrome
papillon-lefèvre syndrome
primary effusion lymphoma
proteus syndrome
severe combined immunodeficiency
sneddon syndrome
waldenström macroglobulinemia
werner syndrome
wiskott-aldrich syndrome
You can validate or delete this automatically detected symptom
Validate the Symptom
Delete the Symptom