Malignant perivascular epithelioid cell tumor of the gallbladder: a case report and review of literature.

[lymphangioleiomyomatosis]

Perivascular epithelioid cell tumors are rare mesenchymal neoplasms composed of histologically and immunohistochemically distinctive perivascular epithelioid cells . The perivascular epithelioid cell tumor family includes angiomyolipoma , clear cell sugar tumor of the lung , lymphangioleiomyomatosis , clear cell myomelanocytic tumor of the falciform ligament /ligamentum teres , and rare clear cell tumors of other anatomic sites . Perivascular epithelioid cell tumors have been reported previously in various sites , but to our knowledge not in the gallbladder . We report here , for the first time , a malignant perivascular epithelioid cell tumor arising in the gallbladder .