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Dendritic fibromyxolipoma: a variant of spindle cell lipoma with extensive myxoid change, with cytogenetic evidence.
[liposarcoma]
Dendritic
fibromyxolipoma
(
DFML
)
,
a
rare
,
recently
described
distinct
benign
soft
tissue
tumor
,
has
many
clinicopathological
features
reminiscent
of
spindle
cell
lipoma
and
solitary
fibrous
tumor
with
myxoid
change
.
It
is
distinguished
histologically
from
both
entities
by
the
presence
of
spindle
and
stellate
cells
with
dendritic
cytoplasmic
prolongations
,
prominent
myxoid
stroma
with
abundant
keloidal
collagen
and
occasional
small
plexiform
vascular
proliferation
.
We
describe
a
case
of
histologically
confirmed
DFML
of
the
left
shoulder
in
a
67
-
year
-old
male
,
in
which
subsequent
cytogenetic
analysis
revealed
deletion
involving
13
q
14
.
3
region
in
all
the
tumor
cells
,
typically
detected
in
spindle
cell
lipoma
.
In
the
presence
of
many
clinicopathological
similarities
between
DFML
and
spindle
cell
lipoma
including
chromosomal
abnormalities
,
we
postulate
that
DFML
is
merely
a
rare
variant
of
spindle
cell
lipoma
with
extensive
myxoid
degeneration
,
and
may
not
be
considered
as
a
separate
entity
.
The
possible
differential
diagnosis
and
their
distinguishing
features
are
briefly
discussed
.
Diseases
Validation
Diseases presenting
"tumor cells"
symptom
alpha-thalassemia
carcinoma of the gallbladder
cholangiocarcinoma
cushing syndrome
dedifferentiated liposarcoma
dentin dysplasia
esophageal adenocarcinoma
esophageal carcinoma
esophageal squamous cell carcinoma
hodgkin lymphoma, classical
junctional epidermolysis bullosa
kindler syndrome
liposarcoma
lymphangioleiomyomatosis
pleomorphic liposarcoma
primary effusion lymphoma
severe combined immunodeficiency
triple a syndrome
von hippel-lindau disease
waldenström macroglobulinemia
well-differentiated liposarcoma
werner syndrome
wiskott-aldrich syndrome
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