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[Anesthetic considerations in primary immunodeficiencies].
[]
Primary
immunodeficiencies
are
a
group
of
mostly
hereditary
,
or
congenital
,
disorders
.
Some
cases
,
however
,
show
no
hereditary
pattern
despite
an
evident
familial
distribution
.
The
incidence
of
these
cases
is
variable
and
the
most
frequent
of
them
is
immunoglobulin
A
deficiency
.
Many
are
pediatric
disorders
that
are
occasionally
so
serious
that
the
patient
does
not
survive
the
first
year
of
life
due
to
the
development
of
systemic
infections
.
In
other
cases
,
survival
is
much
longer
and
it
is
possible
to
find
adult
carriers
in
routine
clinical
practice
.
These
are
less
aggressive
cases
that
form
part
of
specific
clinical
syndromes
that
must
be
recognized
so
that
appropriate
anesthetic
management
can
be
planned
.
We
review
the
clinical
characteristics
of
primary
immunodeficiencies
that
may
be
relevant
to
anesthetic
management
in
these
patients
.
