Rare Diseases Symptoms Automatic Extraction

A rare but life-threatening complication of ventriculo-atrial shunt.

[hydrocephalus with stenosis of the aqueduct of sylvius]

Insertion of ventriculoperitoneal and ventriculoatrial shunts is routinely performed. Infarction pneumonia and atrial thrombus formation are described as very rare complications of ventriculoatrial shunts. We present the case of a female patient with ventriculoatrial shunt insertion as long term treatment for aequeductal stenosis who presented with recurrent episodes of dyspnoea, chest pain, and unilateral pleural effusion. Diagnostic evaluation revealed a positive D-dimer test, bilateral basal infiltrates and pleural effusion. Transesophageal echocardiography established the diagnosis of a thrombus in the right atrium. Laboratory testing for thrombophilia revealed a homozygous factor V Leiden mutation. In the following, a shunt revision was performed.

Diseases presenting "pleural effusion" symptom

  • allergic bronchopulmonary aspergillosis
  • cushing syndrome
  • dedifferentiated liposarcoma
  • erdheim-chester disease
  • esophageal carcinoma
  • hydrocephalus with stenosis of the aqueduct of sylvius
  • lymphangioleiomyomatosis
  • pleomorphic liposarcoma
  • primary effusion lymphoma
  • scrub typhus
  • systemic capillary leak syndrome
  • thoracic outlet syndrome
  • waldenström macroglobulinemia
  • wolf-hirschhorn syndrome

This symptom has already been validated