Rare Diseases Symptoms Automatic Extraction

Ventriculo-peritoneal shunt surgery in an infant with double aortic arch, patent ductus arteriosus and atrial septal defect.

[hydrocephalus with stenosis of the aqueduct of sylvius]

Double aortic arch with patent ductus arteriosus and atrial septal defect is an uncommon association. Such complex cardiac lesions may complicate an otherwise normal anesthetic course. We came across a case with aqueductal stenosis and hydrocephalus, scheduled for ventriculo-peritoneal shunt surgery, on an emergent basis. The child was managed successfully. The anesthetic implications of resultant left-to-right shunt with increased intracranial pressure have been described.

Diseases presenting "hydrocephalus" symptom

  • achondroplasia
  • alexander disease
  • canavan disease
  • congenital toxoplasmosis
  • harlequin ichthyosis
  • hirschsprung disease
  • homocystinuria without methylmalonic aciduria
  • hydrocephalus with stenosis of the aqueduct of sylvius
  • krabbe disease
  • monosomy 21
  • proteus syndrome
  • severe combined immunodeficiency
  • sneddon syndrome
  • von hippel-lindau disease
  • wiskott-aldrich syndrome

This symptom has already been validated