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Hydrocephalus in aqueductal stenosis.
[hydrocephalus with stenosis of the aqueduct of sylvius]
The
sylvian
aqueduct
is
the
most
common
site
of
intraventricular
blockage
of
the
cerebro-
spinal
fluid
.
Clinical
aspects
,
neuroradiological
appearance
,
and
treatment
of
hydrocephalus
secondary
to
aqueductal
stenosis
are
specific
.
An
extensive
literature
review
concerning
etiologic
,
pathogenetic
,
clinical
,
and
neuroradiological
aspects
has
been
performed
.
Therapeutic
options
,
prognosis
,
and
intellectual
outcome
are
also
reviewed
.
The
correct
interpretation
of
the
modern
neuroradiologic
techniques
may
help
in
selecting
adequate
treatment
between
the
two
main
options
(
third
ventriculostomy
or
shunting
)
.
In
the
last
decades
,
endoscopic
third
ventriculostomy
has
become
the
first
-line
treatment
of
aqueductal
stenosis
;
however
,
some
issues
,
such
as
the
cause
of
failures
in
well
selected
patients
,
long
-term
outcome
in
infant
treated
with
ETV
,
and
effect
of
persistent
ventriculomegaly
on
neuropsychological
developmental
,
remain
unanswered
.
Diseases
Validation
Diseases presenting
"hydrocephalus"
symptom
achondroplasia
alexander disease
canavan disease
congenital toxoplasmosis
harlequin ichthyosis
hirschsprung disease
homocystinuria without methylmalonic aciduria
hydrocephalus with stenosis of the aqueduct of sylvius
krabbe disease
monosomy 21
proteus syndrome
severe combined immunodeficiency
sneddon syndrome
von hippel-lindau disease
wiskott-aldrich syndrome
This symptom has already been validated