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Unusual mesencephalic developmental venous anomaly causing obstructive hydrocephalus due to aqueductal stenosis.
[hydrocephalus with stenosis of the aqueduct of sylvius]
Developmental
venous
anomalies
(
DVAs
)
are
benign
vascular
malformations
that
rarely
become
symptomatic
.
They
are
anatomical
variations
of
the
venous
drainage
system
and
most
are
incidentally
discovered
.
Mechanical
(
obstruction
and
compression
of
cerebral
and
neural
structures
)
and
flow-related
pathological
mechanisms
have
been
described
in
rare
cases
of
symptomatic
DVAs
.
The
authors
present
the
case
of
a
10
-
month
-old
boy
with
a
mesencephalic
DVA
compressing
the
aqueduct
and
causing
occlusive
hydrocephalus
.
Endoscopic
inspection
confirmed
the
venous
malformation
causing
aqueductal
stenosis
.
The
authors
successfully
performed
endoscopic
third
ventriculostomy
,
resulting
in
decrease
in
the
size
of
the
ventricles
.
At
the
6
-
month
follow-up
after
surgery
,
the
patient
had
significantly
progressed
in
his
psychomotor
development
.
One
year
postsurgery
the
patient
is
doing
fine
,
with
no
neurological
or
developmental
deficits
.
Diseases
Validation
Diseases presenting
"flow-related pathological mechanisms"
symptom
hydrocephalus with stenosis of the aqueduct of sylvius
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