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Phototolerance induced by narrow-band UVB phototherapy in severe erythropoietic protoporphyria.
[erythropoietic protoporphyria]
Erythropoietic
protoporphyria
arises
from
an
inherited
disorder
of
porphyrin
metabolism
which
leads
to
an
accumulation
of
protoporphyrin
IX
in
the
erythropoietic
system
and
other
tissues
.
It
is
characterized
by
cutaneous
photosensitivity
,
usually
difficult
to
keep
under
control
.
Among
the
scant
therapeutic
options
proposed
to
reduce
photosensitivity
in
erythropoietic
protoporphyria
,
narrow
-band
UVB
phototherapy
has
occasionally
been
used
to
induce
sunlight
tolerance
.
We
report
an
adult
case
of
erythropoietic
protoporphyria
with
a
severe
photosensitivity
treated
with
narrow
-band
UVB
that
developed
an
appropriate
sunlight
phototolerance
,
without
adverse
events
during
phototherapy
.
Diseases
Validation
Diseases presenting
"severe photosensitivity"
symptom
erythropoietic protoporphyria
This symptom has already been validated