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Neoplastic and proliferative disorders of the perinephric space.
[erdheim-chester disease]
The
perinephric
space
is
a
well-marginated
central
compartment
of
the
retroperitoneum
,
located
between
the
anterior
and
posterior
pararenal
spaces
.
Various
neoplastic
and
proliferative
disorders
can
affect
the
perinephric
space
,
and
there
is
a
wide
array
of
imaging
findings
.
Although
many
perinephric
lesions
may
extend
directly
from
the
kidney
and
adrenal
gland
,
other
lesions
occur
in
the
perinephric
space
due
to
haematogenous
spread
,
as
part
of
a
systemic
disease
,
or
by
extension
from
an
adjacent
retroperitoneal
compartment
.
Imaging
plays
a
pivotal
role
in
the
diagnosis
of
perinephric
diseases
,
as
many
of
the
disease
processes
affecting
this
space
will
not
result
in
clinical
signs
or
symptoms
until
the
disease
is
at
an
advanced
stage
.
Despite
the
often
shared
non-
specific
clinical
and
imaging
findings
among
these
disease
processes
,
application
of
a
categorical
differential
diagnosis
based
on
the
imaging
characteristics
will
serve
to
narrow
the
differential
diagnosis
and
direct
further
evaluation
and
treatment
.
In
this
article
,
the
lesions
have
been
categorized
as
soft
-tissue
rind
[
nephroblastomatosis
,
fibrosis
,
Erdheim-
Chester
disease
(
ECD
)
,
extramedullary
haematopoiesis
,
lymphoma
,
infiltrating
metastases
]
,
focal
solid
lesions
(
extension
of
renal
or
adrenal
malignancies
,
melanoma
metastases
,
treated
lymphoma
)
,
fat-containing
lesions
(
angiomyolipoma
,
liposarcoma
,
myelolipoma
)
,
and
cystic
lesions
(
lymphangiomas
,
abscesses
)
.
The
aim
of
this
article
is
to
demonstrate
and
describe
the
key
imaging
features
of
several
neoplastic
and
proliferative
disorders
that
affect
the
perinephric
space
.
Diseases
Validation
Diseases presenting
"many perinephric lesions"
symptom
erdheim-chester disease
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