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Inherited epidermolysis bullosa: Case report of finger localization.
[dystrophic epidermolysis bullosa]
Inherited
epidermolysis
bullosa
is
a
rare
condition
that
often
present
at
birth
with
skin
blisters
and
erosions
.
They
are
associated
with
defective
cohesion
of
the
dermis
and
epidermis
.
There
are
3
principal
types
:
Simple
,
junctional
and
dystrophic
.
The
severity
of
the
condition
is
quite
variable
.
The
most
severe
forms
are
incompatible
with
life
.
The
most
common
types
in
our
country
are
the
severe
ones
such
as
the
Hallopeau
-
Siemens
subtype
.
Hands
and
mucosal
areas
can
develop
synechia
.
We
report
here
a
case
of
dystrophic
epidermolysis
bullosa
in
a
27
-
year
-old
woman
whose
finger
lesion
was
managed
surgically
.
This
treatment
consisted
of
complete
removal
of
constrictions
and
adhesions
,
accompanied
by
use
of
a
Hueston
flap
and
skin
graft
to
repair
the
tissue
deficit
.
The
patient
's
clinical
course
required
several
repeat
operations
.
This
surgery
allowed
the
possible
total
loss
of
hand
function
to
be
delayed
but
the
inevitable
progression
of
the
illness
made
the
treatment
somewhat
disappointing
.
Psychosocial
implications
are
very
significant
in
our
setting
.
