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A random Abstract
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Retroperitoneal liposarcoma with leiomyosarcomatous differentiation.
[dedifferentiated liposarcoma]
We
herein
describe
a
60
-
year
-old
Japanese
man
with
a
giant
retroperitoneal
liposarcoma
undergoing
leiomyosarcomatous
differentiation
.
He
was
admitted
to
our
hospital
because
of
a
5
-
month
history
of
dysphagia
and
abdominal
distention
.
Abdominal
computed
tomography
showed
a
giant
tumor
that
occupied
the
entire
retroperitoneal
space
.
The
majority
of
the
mass
was
lipomatous
and
low
density
;
both
a
heterogenous
and
solid
mass
were
also
present
.
A
giant
retroperitoneal
liposarcoma
was
diagnosed
,
and
tumor
resection
was
performed
.
At
surgery
,
the
tumor
was
mostly
isolated
from
the
retroperitoneum
and
other
organs
.
Histopathologically
,
the
tumor
comprised
well-differentiated
and
dedifferentiated
liposarcoma
with
heterologous
differentiation
of
the
leiomyosarcomatous
components
,
which
is
a
rare
phenomenon
in
liposarcoma
.
The
patient
was
alive
3
years
after
the
first
treatment
,
although
he
has
had
3
local
recurrences
(
approximately
one
recurrence
yearly
)
and
has
been
treated
by
repeated
resection
and
radiotherapy
.
Diseases
Validation
Diseases presenting
"dysphagia"
symptom
alexander disease
cadasil
cushing syndrome
dedifferentiated liposarcoma
dystrophic epidermolysis bullosa
epidermolysis bullosa simplex
esophageal adenocarcinoma
esophageal carcinoma
esophageal squamous cell carcinoma
familial hypocalciuric hypercalcemia
inclusion body myositis
kindler syndrome
liposarcoma
locked-in syndrome
neuralgic amyotrophy
oligodontia
triple a syndrome
well-differentiated liposarcoma
This symptom has already been validated