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[Urticaria pigmentosa: two different clinical presentations in pediatric patients].
[cutaneous mastocytosis]
Urticaria
pigmentosa
(
UP
)
is
the
most
frequent
clinical
feature
of
cutaneous
mastocytosis
.
It
usually
begins
in
a
bimodal
way
:
a
peak
of
incidence
from
birth
to
the
age
of
3
and
the
other
one
between
2
(
nd
)
and
6
(
th
)
decades
of
life
.
Darier
's
sign
is
constant
over
the
affected
skin
without
affecting
the
surrounding
skin
.
When
UP
starts
early
,
it
has
a
good
prognosis
disappearing
into
adolescence
,
while
late
onset
is
often
associated
with
persistent
or
systemic
involvement
.
This
article
reports
two
cases
of
UP
,
one
with
the
classic
description
of
the
disease
and
the
other
with
an
unusual
clinical
presentation
,
prompting
the
pediatrician
to
incorporate
both
forms
as
different
manifestations
of
the
same
entity
.
