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[General anesthesia for a boy with Wolf-Hirschhorn syndrome].
[wolf-hirschhorn syndrome]
Wolf-
Hirschhorn
syndrome
(
WHS
)
is
a
rare
chromosomal
abnormality
in
which
there
is
deletion
of
the
short
arm
of
chromosome
no
.
4
.
Features
of
the
condition
include
severe
psychomotor
retardation
,
characteristic
facies
and
various
congenital
midline
fusion
anomalies
.
We
report
the
anesthetic
management
in
a
6
-
year
-old
boy
with
WHS
,
scheduled
for
renal
biopsy
under
general
anesthesia
.
Anesthesia
was
induced
and
maintained
with
sevoflurane
and
nitrous
oxide
in
oxygen
.
Mask
ventilation
was
performed
easily
.
After
establishment
of
mask
ventilation
,
laryngeal
mask
airway
(
LMA
)
was
inserted
smoothly
without
muscle
relaxant
and
an
adequate
airway
was
established
with
a
LMA
.
He
has
episodes
of
transient
deterioration
in
renal
function
with
physical
stress
.
To
decrease
renal
effects
of
perioperative
stress
,
transversus
abdominis
plane
(
TAP
)
block
and
intravenous
patient
controlled
analgesia
(
IV-
PCA
)
were
administered
for
postoperative
analgesia
.
The
operation
ended
without
any
complications
.
Anesthetic
emergence
was
rapid
and
he
had
no
pain
and
decline
in
renal
function
.