Rare Diseases Symptoms Automatic Extraction

Palmar well differentiated spindle cell liposarcoma: presentation of a rare tumor at a rare site.

[well-differentiated liposarcoma]

The most common soft tissue sarcomas of hand are epitheloid sarcomas, synovial sarcomas and malignant fibrous histiocytomas which are high grade, aggressive tumors. Liposarcomas of the hand are extremely rare and to the best of our knowledge less than 20 cases have been reported so far in the literature. Well differentiated spindle cell liposarcoma is an extremely rare subtype of well differentiated liposarcoma/atypical lipomatous tumor which is different from the other subtypes clinicopathologically, genetically and prognostically. Palmar localization of this rare variant of liposarcoma at this site makes ours only the second case reported in the world literature so far. This recently described entity is low grade lesion and the hand surgeons need to adopt a less aggressive approach in the treatment of this subtype.

Diseases presenting "second case" symptom

  • allergic bronchopulmonary aspergillosis
  • canavan disease
  • coats disease
  • cutaneous mastocytosis
  • esophageal adenocarcinoma
  • fabry disease
  • holt-oram syndrome
  • junctional epidermolysis bullosa
  • legionellosis
  • malignant atrophic papulosis
  • omenn syndrome
  • pleomorphic liposarcoma
  • primary hyperoxaluria type 1
  • proteus syndrome
  • von hippel-lindau disease
  • well-differentiated liposarcoma
  • werner syndrome
  • wolf-hirschhorn syndrome
  • x-linked adrenoleukodystrophy

You can validate or delete this automatically detected symptom