Dedifferentiated liposarcoma of the spermatic cord with a hemangioendothelioma-like component: a case report and review of the literature.

[well-differentiated liposarcoma]

Atypical lipomatous tumor or well-differentiated liposarcoma /dedifferentiated liposarcoma (DDLPS ) is the most frequent subtype of malignant adipocytic tumor . This tumor typically presents in late adult life , most commonly in the retroperitoneum , extremities , or spermatic cord . It has been reported that the dedifferentiated component consists mainly of high -grade sarcoma , including undifferentiated pleomorphic sarcoma , fibrosarcoma , and myxofibrosarcoma , and it has been recently reported that the dedifferentiated component can be also made up of a low -grade sarcomatous component . Therefore , the dedifferentiated areas exhibit a wide morphological spectrum that commonly includes fibroblastic /myofibroblastic and fibrohistiocytic tumors but very rarely includes vascular tumors . We present here the first reported case of DDLPS with a hemangioendothelioma-like component in the spermatic cord .