Rare Diseases Symptoms Automatic Extraction

Retroperitoneal amyloidosis as the presenting manifestation of Waldenstrom's macroglobulinaemia.

[waldenström macroglobulinemia]

Retroperitoneal amyloidosis has been described in a few case reports and is typically a secondary manifestation of inflammation or malignancy. We present the case of a 69-year-old man who presented with a large pleural effusion and an incidental retroperitoneal mass in the CT imaging. Further investigation confirmed the diagnosis of amyloid amyloidosis involving the retroperitoneum as well as a concurrent Waldenstrom's macroglobulinaemia. Chemotherapy consistent of drugs active against both the lymphoid and plasma cell components of the disease is the proposed therapy for Waldenstrom's macroglobulinaemia in those patients amenable to receive chemotherapy and can make a difference in the survival.

Diseases presenting "pleural effusion" symptom

  • allergic bronchopulmonary aspergillosis
  • cushing syndrome
  • dedifferentiated liposarcoma
  • erdheim-chester disease
  • esophageal carcinoma
  • hydrocephalus with stenosis of the aqueduct of sylvius
  • lymphangioleiomyomatosis
  • pleomorphic liposarcoma
  • primary effusion lymphoma
  • scrub typhus
  • systemic capillary leak syndrome
  • thoracic outlet syndrome
  • waldenström macroglobulinemia
  • wolf-hirschhorn syndrome

This symptom has already been validated