Hemorrhagic intramedullary hemangioblastoma of the cervical spinal cord presenting with acute-onset quadriparesis: Case report and review of the literature.

[von hippel-lindau disease]

Context Hemangioblastomas of the spinal cord are uncommon vascular tumors . Patients commonly present with subtle neurologic findings that are thought to represent growth of the lesion over time . Hemorrhage of an intramedullary hemangioblastoma presenting as acute neurologic deficit is an extremely rare occurrence . Although the cervical spine is the most common location for hemangioblastoma of the spinal cord , there have been no previously published cases in the literature of intramedullary hemorrhage from such a lesion . Findings A 22 -year -old woman with a previously undiagnosed spinal cord hemangioblastoma presented with sudden-onset dense quadriparesis due to intramedullary hemorrhage in the cervical spinal cord . The patient did not have any clinical findings of von -Hippel Lindau disease . Laminoplasty from C 5 to T 2 and posterior midline myelotomy for resection of the intramedullary tumor with hematoma evacuation were completed without complication . Conclusion Intramedullary hemangioblastoma of the spinal cord is uncommon , and hemorrhage from a cervical spinal cord lesion has not previously been reported . Symptoms from these usually indolent lesions are commonly associated with tumor growth , edema , or associated syrinx , whereas devastating acute neurologic deficit from hemorrhage is exceedingly rare . Microsurgical resection should be done in cases of symptomatic lesions and considered in isolated symptomatic lesions without the known diagnosis of von Hippel-Lindau disease .

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von hippel-lindau disease

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