Achalasia--alacrima--ACTH insensitivity syndrome (Triple A syndrome).

[triple a syndrome]

Triple A syndrome is characterized by achalasia of the cardia , alacrima , adrenocorticotrophic hormone (ACTH ) resistant adrenal insufficiency and progressive neurological abnormalities including autonomic nervous dysfunction . An 8 -year -old girl presented to the pediatric intensive care unit with sudden loss of consciousness and was diagnosed subsequently to have this condition . The authors present this condition since it is easily treatable and can be fatal if undiagnosed .