Neurogenic thoracic outlet syndrome associated with cervical rib.

[thoracic outlet syndrome]

A true neurogenic thoracic outlet syndrome (TOS ) associated with a cervical rib is considered extremely rare . The authors present their experience with 5 cases of true neurogenic TOS associated with a cervical rib . All patients were female and had a cervical rib confirmed radiographically pre-operatively . Average age was 34 ,8 years . Although all patients had been treated with several combinations of diverse drugs and a rehabilitation program before referral to surgery , all described their pain as intense and debilitating before surgical treatment . All patients had pre-operative electromyographic abnormalities . Patients were operated on via a supraclavicular approach and the cervical rib was resected . No intra-operative or postoperative complications were noted . Two years postoperatively , all patients mentioned improvement . However , only 2 were symptomless , and on no medication . In one patient there was significant improvement , and in the remaining 2 patients some residual pain persisted that had to be dealt with pharmacologically . All patients were able to resume their daily life activities . Recovery was poorer in the 2 patients that had been referred to surgery after a longer period of time since the beginning of symptoms .

Diseases
Validation

Diseases presenting "pain" symptom

achondroplasia

acute rheumatic fever

adrenal incidentaloma

adrenomyeloneuropathy

aniridia

aromatase deficiency

carcinoma of the gallbladder

cholangiocarcinoma

coats disease

congenital diaphragmatic hernia

congenital toxoplasmosis

cushing syndrome

cutaneous mastocytosis

cystinuria

dedifferentiated liposarcoma

dentin dysplasia

dracunculiasis

dystrophic epidermolysis bullosa

epidermolysis bullosa simplex

erdheim-chester disease

erythropoietic protoporphyria

esophageal adenocarcinoma

esophageal carcinoma

esophageal squamous cell carcinoma

fabry disease

familial mediterranean fever

focal myositis

hirschsprung disease

hodgkin lymphoma, classical

holt-oram syndrome

junctional epidermolysis bullosa

kabuki syndrome

kindler syndrome

lamellar ichthyosis

liposarcoma

locked-in syndrome

lymphangioleiomyomatosis

malignant atrophic papulosis

neuralgic amyotrophy

oligodontia

oral submucous fibrosis

papillon-lefèvre syndrome

phenylketonuria

pleomorphic liposarcoma

primary hyperoxaluria type 1

proteus syndrome

pyomyositis

scrub typhus

sneddon syndrome

systemic capillary leak syndrome

thoracic outlet syndrome

trochlear dysplasia

typhoid

von hippel-lindau disease

waldenström macroglobulinemia

well-differentiated liposarcoma

wolf-hirschhorn syndrome

This symptom has already been validated