Rare Diseases Symptoms Automatic Extraction
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A random Abstract
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Systemic capillary leak syndrome.
[systemic capillary leak syndrome]
A
40
-
year
-old
woman
was
referred
to
our
hospital
with
severe
hypovolemic
shock
and
anasarca
.
The
laboratory
findings
showed
marked
hemoconcentration
and
a
decrease
in
total
serum
protein
with
the
presence
of
monoclonal
IgG-lambda
.
She
had
had
a
similar
episode
of
generalized
edema
2
years
previously
.
We
diagnosed
the
patient
as
having
typical
systemic
capillary
leak
syndrome
(
SCLS
)
and
she
improved
gradually
after
infusion
of
albumin
-containing
fluid
.
SCLS
is
a
very
rare
condition
caused
by
unexplained
episodic
capillary
hyperpermeability
.
Its
treatment
has
remained
largely
supportive
and
the
prognosis
is
generally
poor
.
Awareness
of
SCLS
is
necessary
for
improvement
of
the
outcome
.