Rare Diseases Symptoms Automatic Extraction
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Systemic capillary leak syndrome presenting as recurrent shock.
[systemic capillary leak syndrome]
To
report
a
case
of
systemic
capillary
leak
syndrome
(
SCLS
)
in
a
child
.
Case
report
.
Pediatric
intensive
care
unit
.
A
6
-
yr
-old
girl
was
admitted
twice
to
the
pediatric
intensive
care
unit
,
at
a
10
-
month
interval
,
in
severe
shock
with
important
edema
.
The
patient
presented
with
acute
symptoms
of
abdominal
pain
,
vomiting
,
and
syncope
in
the
hour
preceding
the
shock
.
During
both
episodes
necessary
management
included
aggressive
intravenous
fluid
rehydration
,
mechanical
ventilation
,
and
use
of
inotropes
/
vasopressors
.
Suspicion
of
a
lower
limb
fasciitis
necessitated
surgical
exploration
,
but
pathology
reports
were
negative
on
both
occasions
revealing
only
subcutaneous
tissue
edema
.
The
patient
recovered
within
24
hrs
on
both
episodes
.
Investigation
ruled
out
cardiogenic
shock
and
septic
shock
due
to
bacterial
etiology
.
On
the
first
episode
,
a
nasopharyngeal
aspirate
was
positive
for
influenza
A
(
H
3
N
2
)
by
both
viral
immunofluorescence
and
culture
.
The
presumed
diagnosis
was
toxic
shock
syndrome
associated
with
influenza
virus
.
On
the
second
episode
,
all
bacterial
and
virology
cultures
remained
negative
.
Hypovolemic
shock
was
suspected
,
but
there
was
no
history
of
dehydration
,
bleeding
,
or
gastrointestinal
losses
(
persistent
vomiting
or
diarrhea
)
.
Noninfectious
causes
of
hypovolemic
shock
with
edema
were
ruled
out
,
leading
us
to
believe
that
she
suffered
from
SCLS
.
Although
well
described
in
the
adult
literature
,
there
have
been
few
reports
of
SCLS
in
pediatric
patients
.
SCLS
should
be
considered
in
the
differential
diagnosis
of
recurrent
hypovolemic
shock
without
identifiable
cause
.
The
only
therapeutic
intervention
is
to
obtain
vascular
access
when
initial
manifestations
occur
and
give
aggressive
fluid
reanimation
.
Diseases
Validation
Diseases presenting
"edema"
symptom
acute rheumatic fever
adrenomyeloneuropathy
aniridia
cadasil
canavan disease
classical phenylketonuria
coats disease
congenital toxoplasmosis
cushing syndrome
cutaneous mastocytosis
erythropoietic protoporphyria
esophageal carcinoma
fabry disease
familial mediterranean fever
focal myositis
harlequin ichthyosis
homocystinuria without methylmalonic aciduria
inclusion body myositis
lamellar ichthyosis
liposarcoma
lymphangioleiomyomatosis
malignant atrophic papulosis
pleomorphic liposarcoma
systemic capillary leak syndrome
trochlear dysplasia
von hippel-lindau disease
waldenström macroglobulinemia
This symptom has already been validated