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[Recurrent unexplained lipothymia: do not forget the capillary leak syndrome].
[systemic capillary leak syndrome]
Systemic
capillary
leak
syndrome
(
SCLS
)
is
a
rare
disorder
characterized
by
recurrent
spontaneous
episodes
of
hypovolaemic
shock
due
to
marked
plasma
shifts
from
the
intravascular
to
the
extravascular
space
.
It
presents
as
the
characteristic
triad
of
hypotension
,
haemoconcentration
and
hypoalbuminemia
.
We
describe
a
patient
with
SCLS
with
recurrent
lipothymia
who
presented
first
with
delayed
oedema
that
was
thought
to
be
due
to
orlistat
treatment
.
On
the
second
episode
the
patient
was
seen
with
a
pulmonary
hypertension
when
plasma
came
back
into
vessels
.
On
the
third
time
the
characteristic
triad
led
to
the
diagnosis
of
SCLS
.
SCLS
should
be
considered
in
the
differential
diagnosis
of
recurrent
hypovolemic
shock
without
identifiable
cause
.
Nevertheless
,
symptoms
may
be
restricted
to
sole
lipothymia
or
transient
oedema
or
delayed
hypoalbuminemia
rendering
the
diagnosis
difficult
.
Diseases
Validation
Diseases presenting
"hypotension"
symptom
achondroplasia
adrenal incidentaloma
congenital adrenal hyperplasia
congenital diaphragmatic hernia
cutaneous mastocytosis
fabry disease
familial mediterranean fever
primary effusion lymphoma
scrub typhus
systemic capillary leak syndrome
thoracic outlet syndrome
typhoid
This symptom has already been validated