Rare Diseases Symptoms Automatic Extraction
Home
A random Abstract
Our Project
Our Team
Idiopathic systemic capillary leak syndrome (SCLS): case report and systematic review of cases reported in the last 16 years.
[systemic capillary leak syndrome]
'
Idiopathic
systemic
capillary
leak
syndrome
(
SCLS
)
,
or
Clarkson
's
disease
is
an
unusual
entity
first
described
45
years
ago
.
It
presents
with
recurrent
episodes
of
shock
due
to
leakage
of
the
plasma
,
which
is
reflected
by
accompanying
hemo-concentration
,
hypo-albuminemia
and
edema
.
We
report
the
case
of
a
young
man
with
multiple
episodes
of
shock
with
generalized
edema
and
pleural
effusion
.
An
initial
diagnosis
of
sepsis
was
made
,
but
the
lack
of
fever
and
absence
of
a
demonstrable
organism
or
source
led
to
a
revision
of
diagnosis
to
SLCS
.
The
last
review
of
this
syndrome
which
analyzed
24
cases
was
published
in
1990
.
Since
then
,
75
more
cases
have
been
reported
.
This
article
reviews
these
cases
.
Diseases
Validation
Diseases presenting
"recurrent episodes"
symptom
acute rheumatic fever
adrenomyeloneuropathy
benign recurrent intrahepatic cholestasis
child syndrome
cholangiocarcinoma
cystinuria
familial mediterranean fever
hydrocephalus with stenosis of the aqueduct of sylvius
kabuki syndrome
neuralgic amyotrophy
pyruvate dehydrogenase deficiency
systemic capillary leak syndrome
triple a syndrome
You can validate or delete this automatically detected symptom
Validate the Symptom
Delete the Symptom