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A case of idiopathic systemic capillary leak syndrome with high serum levels of G-CSF on exacerbation.
[systemic capillary leak syndrome]
Systemic
capillary
leak
syndrome
(
SCLS
)
is
a
life-threatening
disorder
which
presents
with
periodic
episodes
of
hypovolemic
shock
,
due
to
plasma
leakage
to
the
extra
-
vascular
space
reflected
by
accompanying
hypoalbuminemia
,
hemoconcentration
and
edema
often
with
associated
monoclonal
gammopathy
.
We
describe
a
28
-
year
-old
woman
with
SCLS
who
required
aggressive
fluid
resuscitation
and
was
successfully
treated
with
corticosteroid
,
terbutaline
,
and
theophylline
.
At
exacerbation
,
the
levels
of
serum
granulocyte
colony-stimulating
factor
(
G-CSF
)
were
increased
.
Thus
,
G-CSF
might
play
an
important
role
and
can
be
a
useful
biomarker
for
the
severity
of
attacks
in
SCLS
.
Diseases
Validation
Diseases presenting
"edema"
symptom
acute rheumatic fever
adrenomyeloneuropathy
aniridia
cadasil
canavan disease
classical phenylketonuria
coats disease
congenital toxoplasmosis
cushing syndrome
cutaneous mastocytosis
erythropoietic protoporphyria
esophageal carcinoma
fabry disease
familial mediterranean fever
focal myositis
harlequin ichthyosis
homocystinuria without methylmalonic aciduria
inclusion body myositis
lamellar ichthyosis
liposarcoma
lymphangioleiomyomatosis
malignant atrophic papulosis
pleomorphic liposarcoma
systemic capillary leak syndrome
trochlear dysplasia
von hippel-lindau disease
waldenström macroglobulinemia
This symptom has already been validated