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A case of idiopathic systemic capillary leak syndrome with high serum levels of G-CSF on exacerbation.
[systemic capillary leak syndrome]
Systemic
capillary
leak
syndrome
(
SCLS
)
is
a
life-threatening
disorder
which
presents
with
periodic
episodes
of
hypovolemic
shock
,
due
to
plasma
leakage
to
the
extra
-
vascular
space
reflected
by
accompanying
hypoalbuminemia
,
hemoconcentration
and
edema
often
with
associated
monoclonal
gammopathy
.
We
describe
a
28
-
year
-old
woman
with
SCLS
who
required
aggressive
fluid
resuscitation
and
was
successfully
treated
with
corticosteroid
,
terbutaline
,
and
theophylline
.
At
exacerbation
,
the
levels
of
serum
granulocyte
colony-stimulating
factor
(
G-CSF
)
were
increased
.
Thus
,
G-CSF
might
play
an
important
role
and
can
be
a
useful
biomarker
for
the
severity
of
attacks
in
SCLS
.